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The Middle East and North Africa Diagnosis and Management Guidelines for Inborn Errors of Immunity

Journal of Allergy and Clinical Immunology in Practice · Ocak 2023

Özet
Human inborn errors of immunity (IEI) are a group of 485 distinct genetic disorders affecting children and adults. Signs and symptoms of IEI are heterogeneous, and accurate diagnosis can be challenging and depends on the available human expertise and laboratory resources. The Middle East and North Africa (MENA) region has an increased prevalence of IEI because of the high rate of consanguinity with a predominance of autosomal recessive disorders. This area also exhibits more severe disease phenotypes compared with other regions, probably due to the delay in diagnosis. The MENA-IEI registry network has designed protocols and guidelines for the diagnosis and treatment of IEI, taking into consideration the variable regional expertise and resources. These guidelines are primarily meant to improve the care of patients within the region, but can also be followed in other regions with similar patient populations.
64 atıf Ocak 2023 DOI
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YÖKSİS Kayıtları
The Middle East and North Africa Diagnosis and Management Guidelines for Inborn Errors of Immunity
Elsevier BV · 2022 SCI
Prof. Dr. HASİBE ARTAÇ →
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The Middle East and North Africa Diagnosis and Management Guidelines for Inborn Errors of Immunity
2022 ISSN: 2213-2198 SCI Q1
Prof. Dr. HASİBE ARTAÇ →

Makale Bilgileri

Toplam Atıf 64 atıf · Scopus
ISSN22132198
Yayın TarihiOcak 2023
Cilt / Sayfa11 · 158-180.e11
Erişim🔓 Açık Erişim

Kurumlar

Al-Sabah Hospital
Kuwait
American University of Beirut
Beirut Lebanon
Ankara Üniversitesi
Ankara Turkey
Başkent Üniversitesi
Ankara Turkey
Boston Children's Hospital
Boston United States
Bursa Uludağ Üniversitesi
Bursa Turkey
Centre Hospitalier et Universitaire de Béni-Messous, Algiers
Algiers Algeria
College of Medicine Alfaisal University
Riyadh Saudi Arabia
College of Medicine and Health Sciences United Arab Emirates University
Al Ain United Arab Emirates
Dr. Behcet Uz Children's Hospital
Izmir Turkey
Faculty of Medicine
Cairo Egypt
Faculty of Medicine
Mansoura Egypt
Faculty of Medicine, Ain Shams University
Cairo Egypt
Gilbert and Rose-Marie Chagoury School of Medicine
Byblos Lebanon
Hacettepe Üniversitesi
Ankara Turkey
Hamad Medical Corporation
Doha Qatar
Institut Pasteur - Alger
Algiers Algeria
Institut Pasteur de Tunis
Tunis Tunisia
Istanbul Jeffrey Modell Diagnostic and Research Center for Primary Immunodeficiencies
Istanbul Turkey
İstanbul University-Cerrahpaşa Cerrahpaşa Faculty of Medicine
Istanbul Turkey
Karolinska Universitetssjukhuset
Stockholm Sweden
King Faisal Specialist Hospital & Research Centre
Riyadh Saudi Arabia
King Saud bin Abdulaziz University for Health Sciences
Riyadh Saudi Arabia
Kuwait University
Kuwait City Kuwait
Laboratoire de Recherche en Immunologie Clinique, Inflammation et Allergie
Casablanca Morocco
Marmara Üniversitesi Tip Fakültesi
Istanbul Turkey
Mofid Children's Hospital, Tehran
Tehran Iran
Necmettin Erbakan Üniversitesi
Meram Turkey
Queen Rania Children's Hospital
Amman Jordan
Research Center for Immunodeficiencies
Tehran Iran
Royal Hospital
Muscat Oman
Selçuk Tip Fakültesi
Konya Turkey
Sidra Medicine
Doha Qatar
Sultan Qaboos University Hospital
Muscat Oman
Tawam Hospital
Abu Dhabi United Arab Emirates
Universal Scientific Education and Research Network (USERN)
Tehran Iran
Université d’Alger 1
Algiers Algeria

Havuzumuzdaki Atıflar 0

Bu makaleye, sistemimizdeki Scopus veritabanında bulunan 0 makale atıf yapmıştır. Scopus genel atıf sayısı: 64.

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Scimago Dergi (ISSN Eşleşmesi)
Journal of Allergy and Clinical Immunology: In Practice
Q1
SJR Skoru1,773
H-Index117
YayıncıAmerican Academy of Allergy, Asthma and Immunology
ÜlkeUnited States
Immunology and Allergy (Q1)
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Metrikler

64
Atıf

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