Aim: Mucous membrane pemphigoid (MMP) is a chronic autoimmune subepithelial blistering disorder that primarily affects mucosal surfaces. Laryngeal involvement is uncommon but clinically important, as it may result in progressive scarring and severe airway obstruction. Because of its rarity, the diagnosis can be easily overlooked, and the number of reported cases in the literature remains limited. In this case report, we present the clinical findings, diagnostic approach, treatment strategy, and follow-up of a patient with laryngeal MMP. By sharing this case, we aim to contribute to the limited body of evidence on this rare presentation and highlight the importance of early recognition and appropriate management in preventing life-threatening complications.